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TYVASO and TYVASO DPI are approved for the treatment of pulmonary hypertension associated with interstitial lung disease (PH-ILD; WHO Group 3) to improve the ability to exercise.

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It’s important to be checked for PH regularly because PH can appear at any time as your ILD progresses.

PH-ILD stages of progression
PH-ILD stages of progression

ILD causes lung tissue to become stiff, making it harder to breathe and get oxygen into the blood.

PH-ILD stages of progression

PH causes the blood vessels in the lungs to become narrow, making it harder for blood to flow and causing pressure to increase.

PH-ILD stages of progression

The heart has to work harder to push blood through the lungs, which weakens or damages the heart.

Treatment with TYVASO can reduce the risk of PH-ILD getting worse.

How common is PH in patients with ILD?

PH is sometimes present even when someone is first diagnosed with interstitial lung disease, such as IPF.