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TYVASO and TYVASO DPI are approved for the treatment of pulmonary hypertension associated with interstitial lung disease (PH-ILD; WHO Group 3) to improve the ability to exercise.

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Uncover helpful clues in your routine ILD tests

If the results of your regular ILD tests are worsening, they may be indicators of PH. Here are some things your doctor could look for:

Test What it shows Signs of PH your doctor will look for

Pulmonary Function Tests (PFTs)

How well are your lungs working?

  • DLCO <40%
  • Decline in DLCO but little or no change in FVC

Blood Test

How much strain is your heart under?

  • Increased levels of NT-proBNP and BNP

Oxygen Saturation

Is your blood getting enough oxygen?

  • Reduced oxygen in the blood
  • Need (or increased need) for supplemental oxygen

Exercise Capacity Test (6-minute walk test)

How active are you able to be?

  • Reduced distance
  • Increased recovery time
  • More shortness of breath
What it shows
Signs of PH your doctor will look for

BNP=B-type natriuretic peptide; DLCO=diffusing capacity of the lung for carbon monoxide; FVC=forced vital capacity; ILD=interstitial lung disease; NT-proBNP=N-terminal pro–B-type natriuretic peptide; PH=pulmonary hypertension.

Ask your doctor if any of the test results above are changing, and if so, could it be PH?

Your actions are key to being more active.

Get to know the tests your doctor is ordering so you can have informed discussions. Educating yourself about these tests can be the difference in making every conversation more productive, which may ultimately result in you feeling better.

Since PH may appear at any time, checking your test results once is not enough. Be sure to have your doctor check for signs of PH whenever you have testing done.

Your role in helping to identify PH is crucial, as PH can appear at any time.

Had an echo and it didn’t show PH?

Keep asking questions. Echos often don’t indicate PH-ILD, especially in the early stages of PH.


of patients diagnosed* with PH-ILD had an echo that showed a low likelihood of PH

* PH-ILD diagnosis was confirmed with a right heart catheterization (RHC), the required test to diagnose PH-ILD.

An echocardiogram, or “echo,” is less effective for catching PH in the early stages, because changes that happen during the early phase of PH are subtle and not easily seen with echo. Also, existing lung disease can make PH difficult to detect on an echo. So that means you can’t rely on echo alone to detect early signs of PH.

When can an echo be most useful?

  • It can be a useful tool to detect later-stage PH—when it becomes more obvious
  • It can also help detect unhealthy changes in the way the heart is working

Talk to your doctor about the other ILD tests that should be looked at along with an echo.

Ruling PH in or out

A right heart catheterization is required to diagnose PH.

A right heart catheterization, often referred to as a right heart cath, is the only way to definitively diagnose PH. It measures the pressure in your heart and in the blood vessels of your lungs. This can help your doctor understand how well your heart and lungs are working and helps determine next steps in the management of your condition.

Raise the questions. Sign up to receive communications to prepare you for conversations with your doctor.

Here’s a resource that can tell you more about the right heart cath test.

Good news: there is now a treatment that can help.

Be proactive in checking for PH.